A Japanese patient presents with bilateral loss of vision and the red eye shown above. Fluid accumulating behind the retina leads to retinal elevation and predisposes him to a retinal detachment. You also notice the whitening of his eyelashes, white patches on the skin, a history of sterile meningitis, loss of hair, and an 8th nerve palsy. This disease is also seen in the Hispanic population.Challenge: This is a hard one. What is it?
Image is in the public domain.
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2 comments:
chediak-higashi?
Japanese
This is Vogt-Koyanagi-Harada syndrome, the second leading cause of uveitis in Japan (after Behcet’s syndrome). It is presumably autoimmune.
Sources: UpToDate; Wikipedia.
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