This disease is described in a story by Lorrie Moore with the same title as this case. Here is a typical presentation. A four year old African American girl presents with abdominal pain and hematuria. On exam, you find that she is hypertensive and you palpate a firm, nontender, smooth abdominal mass that does not cross the midline. Further workup involves removing a kidney. The pathology is shown below:
You notice the gross specimen shows infiltration by a fleshy tan mass with a pseudocapsule surrounded by areas of hemorrhage and necrosis. The histology shows three cell types.
Challenge: What's the diagnosis here?
1. What three cell types are seen on histology?
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